• Pulmonary Hypertension - PASP >25 mmHg
  • WHO Group 1: PAH (Idiopathic, Inherited, Drug induced, Associated with Connective Tissue Disease, HIV and Schistosomiasis)
  • WHO Group 2: Associated with Left Heart Failure
  • WHO Group 3: Associated with Lung Disease and Chronic Hypoxemia
  • WHO Group 4: Chronic Thromboembolic Pulmonary Hypertension (CTEPH)
  • WHO Group 5: Miscellaneous
  
  

  Posted 03/27/17 09:15:51 AM by Ying Liu

• Interstitial Lung Disease (ILD) Differential
  • Known Causes
    • Drugs - Amiodarone, Nitrofurantoin, Methotrexate
    • Radiation
    • Connective Tissue Disease (RA, Scleroderma, Sjogrens, less commonly SLE)
    • Pneumoconiosis (Coal)
    • Hypersensitivity Pneumonitis
  • Idiopathic
    • Idiopathic Pulmonary Fibrosis (IPF)
    • Non-Specific Interstitial Pneumonia (NSIP)
    • Respiratory Bronchiolitis ILD (RBILD) - smoking-related
    • Cryptogenic Organizing Pneumonia (COP)
  • Granulomatous (Sarcoid)
  • Other (LAM, Pulmonary Alveolar Proteinosis (PAP), PUlmonary Langerhan's Cell Histiocytosis)
  
  

  Posted 03/27/17 09:23:31 AM by Ying Liu

• Cryptogenic Organizing Pneumonia (COP)
  • Rare, 1.1 per 100,000 people
  • Characterized by proliferation of granulation tissue and fibroblasts in alveoli with intraluminal plugs of granulation tissue
  • Present in 5th-6th decade of life
  • Often presents with cough, dyspnea and occasionally fever
  • Treatment is with glucocorticoids, and complete recovery occurs in two-thirds of patients treated with steroids. Recovery can be dramatic, occurring over 1-2 weeks
  
  

  Posted 03/27/17 11:52:42 AM by Ying Liu

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