• Four items on initial evaluation of patient that indicate new diagnosis of ILD
  • Subacute presentation
  • Hypoxemia/impaired A-a gradient
  • Diffuse lung lesions on CXR
  • Restrictive pattern on PFTs
  
  

  Posted 12/13/16 10:46:33 AM by Anna Krigel

• Sarcoidosis - nodular pattern in parenchyma on imaging as opposed to linear pattern
  
  

  Posted 12/13/16 10:47:00 AM by Anna Krigel

• Restrictive Lung Disease
  • Decreased Total Lung Capacity (TLC) on PFTs without evidence of obstruction on FEV1/FVC ratio
  • Three causes
    • Obesity
    • ILD
    • Neuromuscular disease
  
  

  Posted 12/13/16 10:48:11 AM by Anna Krigel

• Four categories of Interstitial Lung Disease
  • Rare - LAM, eosinophilic granuloma
  • Known causes - Occupational exposures, environmental exposures, connective tissue diseases
  • Granulomatous disease - sarcoidosis, hypersensitivity pneumonitis
  • Idiopathic interstitial pneumonas
  
  

  Posted 12/13/16 10:53:19 AM by Anna Krigel

• Idiopathic Interstitial Pneumonias
  • Acute interstitial PNA (AIP) - acute (presentation of one month or less), idiopathic ARDS, very rare
  • Respiratory bronchiolitis-ILD (RB-ILD), desquamative interstitial PNA (DIP) - smoking-related
  • Cryptogenic organizing PNA (COP) - alveolar-filling process, mass-like and nodular in appearance
  • Non-specific interstitial PNA (NSIP) - basilar-predominant process, ground glass opacities and reticular pattern on imaging, 80% of patients will have fibrotic pattern as well, seen in patients with undifferentiated connective tissue disease, SLE, Sjogren's, Systemic sclerosis, and dermatomyositis
  • Usual interstitial PNA/Idiopathic pulmonary fibrosis (UIP/IPF) - basilar predominance, honey-combing pattern, seen in patients with RA 
  
  

  Posted 12/13/16 11:54:15 AM by Anna Krigel

Created by Christopher Kelly
The information on the website does not constitute official guidelines except where explicitly stated.
It is not meant to replace the advice of a health professional.